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Management of Congenital Heart Disease

State of the Art; Part I—Acyanotic Heart Defects

Bibliographic Data

ID15712907
AuthorsP Syamasundar Rao (0000-0002-6382-407X, Memorial Hermann, corresponding author)
Year2019
Volume6
Issue3
Pages42-42
Publication date2019-03-08
Open AccessYes
TypeARTICLE
VenueChildren (JOURNAL)
Journal identifiersISSN: 2227-9067 • E-ISSN: 2227-9067
PublisherMultidisciplinary Digital Publishing Institute (PUBLISHER • CH)
DOI10.3390/children6030042
PMID30857252
OpenAlexW2920971419
LanguageEN
Citations received3
References cited62

In this review management of the most common cyanotic congenital heart defects (CHDs) was discussed; the management of acyanotic CHD was reviewed in Part I of this series. While the need for intervention in acyanotic CHD is by and large determined by the severity of the lesion, most cyanotic CHDs require intervention, mostly by surgery. Different types of tetralogy of Fallot require different types of total surgical corrective procedures, and some may require initial palliation, mainly by modified Blalock-Taussig shunts. Babies with transposition of the great arteries with an intact ventricular septum as well as those with ventricular septal defects (VSD) need an arterial switch (Jatene) procedure while those with both VSD and pulmonary stenosis should be addressed by Rastelli procedure. These procedures may need to be preceded by prostaglandin infusion and/or balloon atrial septostomy in some babies. Infants with tricuspid atresia require initial palliation either with a modified Blalock-Taussig shunt or banding of the pulmonary artery and subsequent staged Fontan (bidirectional Glenn and fenestrated Fontan with extra-cardiac conduit). Neonates with total anomalous pulmonary venous connection are managed by anastomosis of the common pulmonary vein with the left atrium either electively in non-obstructed types or as an emergency procedure in the obstructed types. Babies with truncus arteriosus are treated by surgical closure of VSD along with right ventricle to pulmonary artery conduit. The other defects, namely, hypoplastic left heart syndrome, pulmonary atresia with intact ventricular septum, double-outlet right ventricle, double-inlet left ventricle and univentricular hearts largely require multistage surgical correction. The currently existing medical, trans-catheter and surgical techniques to manage cyanotic CHD are safe and effective and can be performed at a relatively low risk

Cardiology · Catheter · Ductus arteriosus · Heart defect · Heart disease · Intensive care medicine · Intervention (counseling · Lesion · Shunt (medical · Cardiovascular and Diving-Related Complications · Cardiovascular Conditions and Treatments · Congenital Heart Disease Studies · Medicine · Surgery

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    Open Access•P Syamasundar Rao•Children•2019

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Citations per year0.43
Citation span2019 - 2025 (7)
Highly citedNo

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