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Synchronous Cardiac Fibroma and Medulloblastoma in Gorlin Syndrome

A Paradigmatic Case and Narrative Review

Bibliographic Data

ID15717204
AuthorsMarta Molteni (University of Genoa), Gianluca Trocchio (0000-0002-5069-7067, Istituto Giannina Gaslini), Antonio Verrico (0000-0002-4648-4384, Istituto Giannina Gaslini), Maria Derchi (0000-0002-2493-3708, Istituto Giannina Gaslini), Nicola Stagnaro (0000-0003-2845-0591, Istituto Giannina Gaslini), Angela Di Giannatale (0000-0001-8465-3612, Bambino Gesù Children's Hospital), Paola Ghiorzo (0000-0002-3651-8173, Ospedale Policlinico San Martino), Alessia Montaguti (Istituto Giannina Gaslini), Antonia Ramaglia (0000-0003-2998-3322, Istituto Giannina Gaslini), Claudia Milanaccio (0000-0002-8023-643X, Istituto Giannina Gaslini), Gianluca Piccolo (0000-0003-2815-6288, Istituto Giannina Gaslini, corresponding author), Maria Luisa Garrè (0000-0002-9055-3340, Istituto Giannina Gaslini)
LanguageEN
References cited55

In GS patients with concurrent MB and CF, prioritizing MB treatment and adopting a conservative, closely monitored approach to CF can yield excellent long-term outcomes. In children with MB, especially syndromic forms, routine echocardiography is recommended to detect CF. This case underscores the value of multidisciplinary care in managing complex GS presentations

Fibroma · Medulloblastoma · Multidisciplinary approach · Narrative review · Patient care · Value (mathematics · Cardiac tumors and thrombi · Ear and Head Tumors · Vascular Malformations and Hemangiomas

Highly citedNo
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