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Internal Ileal Diversion as Treatment for Progressive Familial Intrahepatic Cholestasis Type 1-Associated Graft Inflammation and Steatosis after Liver Transplantation

Bibliographic Data

ID15718582
AuthorsAnna Maria Kavallar (Innsbruck Medical University), Franka Messner (0000-0003-2100-6914, Universität Innsbruck), Stefan Scheidl (0000-0001-9568-4422, Innsbruck Medical University), Rupert Oberhuber (Universität Innsbruck), Stefan Schneeberger (0000-0002-2619-8639, Innsbruck Medical University), Denise Aldrian (0000-0002-6787-4939, Universität Innsbruck), Valeria Berchtold (0000-0002-6997-3244, Innsbruck Medical University), Murat Şanal (Innsbruck Medical University), Andreas Entenmann (Universität Innsbruck), Simon Straub (Innsbruck Medical University), Anna Gasser (Universität Innsbruck), Andreas Janecke (0000-0001-7155-0315, Universität Innsbruck), Thomas Müller (0000-0003-1225-1483, Universität Innsbruck), Georg F Vogel (0000-0002-2515-4490, Universität Innsbruck, corresponding author)
Year2022
Volume9
Issue12
Pages1964-1964
Publication date2022-12-14
Open AccessYes
TypeARTICLE
VenueChildren (JOURNAL)
Journal identifiersISSN: 2227-9067 • E-ISSN: 2227-9067
PublisherMultidisciplinary Digital Publishing Institute (PUBLISHER • CH)
DOI10.3390/children9121964
PMID36553407
OpenAlexW4311792067
LanguageEN
References cited1

We present three PFIC1 cases for whom SBD to the terminal ileum successfully helped to resolve graft inflammation and steatosis

Cholestasis · Inflammation · Liver transplantation · Progressive familial intrahepatic cholestasis · Steatosis · Drug Transport and Resistance Mechanisms · Liver Disease Diagnosis and Treatment · Medicine · Pediatric Hepatobiliary Diseases and Treatments · Gastroenterology · Internal Medicine · Transplantation

  • Ileal Bile Acid Transporter Inhibition Reduces Post-Transplant Diarrhea and Growth Failure in FIC1 Disease—A Case Report

    Open Access•Johanna Ohlendorf, Imeke Goldschmidt et al.•Children•2022

Highly citedNo

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